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molecular complex
Properties
SUBUNITS: coagulation factor VIII
MOTIF: signal sequence {1-19}
F5/8 type A 1 {20-348}
MOTIF: Plastocyanin-like 1 {20-198}
N-glycosylation site {N60}
cysteine residue {C172}
MODIFICATION: cysteine residue {C198}
cysteine residue {C198}
MODIFICATION: cysteine residue {C172}
Plastocyanin-like 2 {206-348}
N-glycosylation site {N258}
cysteine residue {C267}
MODIFICATION: cysteine residue {C348}
cysteine residue {C348}
MODIFICATION: cysteine residue {C267}
proteolytic site {391-392}
F5/8 type A 2 {399-730}
MOTIF: Plastocyanin-like 3 {399-573}
cysteine residue {C547}
MODIFICATION: cysteine residue {C573}
cysteine residue {C573}
MODIFICATION: cysteine residue {C547}
Plastocyanin-like 4 {583-730}
N-glycosylation site {N601}
cysteine residue {C649}
MODIFICATION: cysteine residue {C730}
cysteine residue {C730}
MODIFICATION: cysteine residue {C649}
proteolytic site {759-760}
B {760-1667}
MOTIF: N-glycosylation site {N776}
N-glycosylation site {N803}
N-glycosylation site {N847}
N-glycosylation site {N919}
N-glycosylation site {N962}
N-glycosylation site {N982}
N-glycosylation site {N1020}
N-glycosylation site {N1024}
N-glycosylation site {N1074}
N-glycosylation site {N1085}
N-glycosylation site {N1204}
N-glycosylation site {N1274}
N-glycosylation site {N1278}
N-glycosylation site {N1301}
N-glycosylation site {N1319}
proteolytic site {1332-1333}
N-glycosylation site {N1431}
N-glycosylation site {N1461}
proteolytic site {1667-1668}
proteolytic site {1708-1709}
F5/8 type A 3 {1713-2040}
MOTIF: Plastocyanin-like 5 {1713-1877}
N-glycosylation site {N1829}
cysteine residue {C1851}
MODIFICATION: cysteine residue {C1877}
cysteine residue {C1877}
MODIFICATION: cysteine residue {C1851}
Plastocyanin-like 6 {1887-2040}
cysteine residue {C1918}
MODIFICATION: cysteine residue {C1922}
cysteine residue {C1922}
MODIFICATION: cysteine residue {C1918}
coagulation factors 5/8 type C domain (FA58C) {2040-2188}
MOTIF: cysteine residue {C2040}
MODIFICATION: cysteine residue {C2188}
N-glycosylation site {N2137}
cysteine residue {C2188}
MODIFICATION: cysteine residue {C2040}
coagulation factors 5/8 type C domain (FA58C) {2193-2345}
MOTIF: cysteine residue {C2193}
MODIFICATION: cysteine residue {C2345}
cysteine residue {C2345}
MODIFICATION: cysteine residue {C2193}
PRECURSOR-FOR: coagulation factor VIIIa
von Willebrand factor
MOTIF: glycosylation site
PEST region
WKS motif
binding site
EFFECTOR-BOUND: coagulation factor VIII
binding site
FOR-BINDING-OF: glycoprotein IIB/IIIA
binding site
FOR-BINDING-OF: platelet glycoprotein 1b
binding site
FOR-BINDING-OF: collagen
cysteine residue
MODIFICATION: cysteine residue
SECRETED-BY: endothelial cell