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1) ==> enzymatic reaction ENZYME: pyruvate carboxylase {MITOCHONDRIA} SUBSTRATE: pyruvate CO2 adenosine triphosphate H2O PRODUCT: oxaloacetate adenosine 5'-diphosphate H2PO4- 2) ==> enzymatic reaction ENZYME: phosphoenolpyruvate carboxykinase {CYTOPLASM} {MITOCHONDRIA} SUBSTRATE: oxaloacetate guanosine triphosphate PRODUCT: phosphoenol-pyruvate guanosine diphosphate CO2 3) ==> enzymatic reaction ENZYME: isocitrate dehydrogenase {MITOCHONDRIAL_MATRIX} SUBSTRATE: isocitrate {MITOCHONDRIAL_MATRIX.2612} NAD {MITOCHONDRIAL_MATRIX.2612} PRODUCT: alpha-ketoglutarate {MITOCHONDRIAL_MATRIX.2612} NADH {MITOCHONDRIAL_MATRIX.2612} CO2 {MITOCHONDRIAL_MATRIX.2612} 4) ==> enzymatic reaction ENZYME: alpha-ketoglutarate dehydrogenase {MITOCHONDRIAL_MATRIX} (2-oxoglutarate dehydrogenase E1 dihydrolipamide acyltransferase E2 lipoamide dehydrogenase -[FAD]) SUBSTRATE: alpha-ketoglutarate {MITOCHONDRIAL_MATRIX.2612} NAD {MITOCHONDRIAL_MATRIX.2612} coenzyme A {MITOCHONDRIAL_MATRIX.2612} PRODUCT: succinyl CoA {MITOCHONDRIAL_MATRIX.2612} CO2 NADH 5) ==> enzymatic reaction ENZYME: carbamoyl phosphate synthase-1 {MITOCHONDRIAL_MATRIX} SUBSTRATE: CO2 NH3 adenosine triphosphate PRODUCT: carbamoyl phosphate {MITOCHONDRIAL_MATRIX.2612} adenosine 5'-diphosphate H2PO4- 6) ==> enzymatic reaction ENZYME: pyrophospho mevalonate decarboxylase SUBSTRATE: 5-pyrophospho mevalonate {CYTOPLASM.1134} adenosine triphosphate PRODUCT: isopentenyl pyrophosphate adenosine 5'-diphosphate CO2 H2PO4- 7) ==> enzymatic reaction ENZYME: phospho-pantothenoyl cysteine decarboxylase SUBSTRATE: 4-phosphopantothenoylcysteine PRODUCT: 4-phospho pantetheine CO2 8) ==> enzymatic reaction ENZYME: aromatic amino-acid decarboxylase SUBSTRATE: tryptophan PRODUCT: tryptamine CO2 9) ==> enzymatic reaction ENZYME: carboxy-lyase SUBSTRATE: indolepyruvate PRODUCT: indoleacetic acid CO2 10) ==> enzymatic reaction ENZYME: dopa decarboxylase SUBSTRATE: 5-hydroxytryptophan PRODUCT: serotonin CO2 11) ==> enzymatic reaction ENZYME: transferase SUBSTRATE: alpha-ketoadipate coenzyme A PRODUCT: glutaryl CoA CO2 12) ==> enzymatic reaction ENZYME: oxidoreductase SUBSTRATE: glutaryl CoA coenzyme A PRODUCT: acetyl-CoA CO2 13) ==> enzymatic reaction ENZYME: trimethyllysine hydroxylase {MITOCHONDRIAL_MATRIX} SUBSTRATE: trimethyllysine alpha-ketoglutarate O2 PRODUCT: beta-OH trimethyllysine succinate {MITOCHONDRIAL_MATRIX.2612} CO2 14) ==> enzymatic reaction ENZYME: gamma-butyrobetaine hydroxylase {CYTOPLASM} SUBSTRATE: gamma-butyrobetaine alpha-ketoglutarate O2 PRODUCT: carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547} succinate {MITOCHONDRIAL_MATRIX.2612} CO2 15) ==> enzymatic reaction ENZYME: carbamoyl phosphate synthase-1 {MITOCHONDRIAL_MATRIX} SUBSTRATE: CO2 NH3 H2O adenosine triphosphate {MITOCHONDRIAL_MATRIX.2612} PRODUCT: carbamoyl phosphate {MITOCHONDRIAL_MATRIX.2612} adenosine 5'-diphosphate {MITOCHONDRIAL_MATRIX.2612} H2PO4- {MITOCHONDRIAL_MATRIX.2612}