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retrieval
1) ==> enzymatic reaction
ENZYME:
pyruvate carboxylase {MITOCHONDRIA}
SUBSTRATE:
pyruvate
CO2
adenosine triphosphate
H2O
PRODUCT:
oxaloacetate
adenosine 5'-diphosphate
H2PO4-
2) ==> enzymatic reaction
ENZYME:
phosphoenolpyruvate carboxykinase {CYTOPLASM} {MITOCHONDRIA}
SUBSTRATE:
oxaloacetate
guanosine triphosphate
PRODUCT:
phosphoenol-pyruvate
guanosine diphosphate
CO2
3) ==> enzymatic reaction
ENZYME:
isocitrate dehydrogenase {MITOCHONDRIAL_MATRIX}
SUBSTRATE:
isocitrate {MITOCHONDRIAL_MATRIX.2612}
NAD {MITOCHONDRIAL_MATRIX.2612}
PRODUCT:
alpha-ketoglutarate {MITOCHONDRIAL_MATRIX.2612}
NADH {MITOCHONDRIAL_MATRIX.2612}
CO2 {MITOCHONDRIAL_MATRIX.2612}
4) ==> enzymatic reaction
ENZYME:
alpha-ketoglutarate dehydrogenase {MITOCHONDRIAL_MATRIX}
(2-oxoglutarate dehydrogenase E1
dihydrolipamide acyltransferase E2
lipoamide dehydrogenase
-[FAD])
SUBSTRATE:
alpha-ketoglutarate {MITOCHONDRIAL_MATRIX.2612}
NAD {MITOCHONDRIAL_MATRIX.2612}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT:
succinyl CoA {MITOCHONDRIAL_MATRIX.2612}
CO2
NADH
5) ==> enzymatic reaction
ENZYME:
carbamoyl phosphate synthase-1 {MITOCHONDRIAL_MATRIX}
SUBSTRATE:
CO2
NH3
adenosine triphosphate
PRODUCT:
carbamoyl phosphate {MITOCHONDRIAL_MATRIX.2612}
adenosine 5'-diphosphate
H2PO4-
6) ==> enzymatic reaction
ENZYME:
pyrophospho mevalonate decarboxylase
SUBSTRATE:
5-pyrophospho mevalonate {CYTOPLASM.1134}
adenosine triphosphate
PRODUCT:
isopentenyl pyrophosphate
adenosine 5'-diphosphate
CO2
H2PO4-
7) ==> enzymatic reaction
ENZYME:
phospho-pantothenoyl cysteine decarboxylase
SUBSTRATE:
4-phosphopantothenoylcysteine
PRODUCT:
4-phospho pantetheine
CO2
8) ==> enzymatic reaction
ENZYME:
aromatic amino-acid decarboxylase
SUBSTRATE:
tryptophan
PRODUCT:
tryptamine
CO2
9) ==> enzymatic reaction
ENZYME:
carboxy-lyase
SUBSTRATE:
indolepyruvate
PRODUCT:
indoleacetic acid
CO2
10) ==> enzymatic reaction
ENZYME:
dopa decarboxylase
SUBSTRATE:
5-hydroxytryptophan
PRODUCT:
serotonin
CO2
11) ==> enzymatic reaction
ENZYME:
transferase
SUBSTRATE:
alpha-ketoadipate
coenzyme A
PRODUCT:
glutaryl CoA
CO2
12) ==> enzymatic reaction
ENZYME:
oxidoreductase
SUBSTRATE:
glutaryl CoA
coenzyme A
PRODUCT:
acetyl-CoA
CO2
13) ==> enzymatic reaction
ENZYME:
trimethyllysine hydroxylase {MITOCHONDRIAL_MATRIX}
SUBSTRATE:
trimethyllysine
alpha-ketoglutarate
O2
PRODUCT:
beta-OH trimethyllysine
succinate {MITOCHONDRIAL_MATRIX.2612}
CO2
14) ==> enzymatic reaction
ENZYME:
gamma-butyrobetaine hydroxylase {CYTOPLASM}
SUBSTRATE:
gamma-butyrobetaine
alpha-ketoglutarate
O2
PRODUCT:
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
succinate {MITOCHONDRIAL_MATRIX.2612}
CO2
15) ==> enzymatic reaction
ENZYME:
carbamoyl phosphate synthase-1 {MITOCHONDRIAL_MATRIX}
SUBSTRATE:
CO2
NH3
H2O
adenosine triphosphate {MITOCHONDRIAL_MATRIX.2612}
PRODUCT:
carbamoyl phosphate {MITOCHONDRIAL_MATRIX.2612}
adenosine 5'-diphosphate {MITOCHONDRIAL_MATRIX.2612}
H2PO4- {MITOCHONDRIAL_MATRIX.2612}