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1) ==> enzymatic reaction
ENZYME: gamma-butyrobetaine hydroxylase {CYTOPLASM}
SUBSTRATE: gamma-butyrobetaine
alpha-ketoglutarate
O2
PRODUCT: carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
succinate {MITOCHONDRIAL_MATRIX.2612}
CO2
2) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
3) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
4) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
5) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
6) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
7) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
8) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
9) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
10) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
11) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
12) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
13) ==> enzymatic reaction
ENZYME: carnitine palmitoyltransferase 1 {INNER_MITOCHONDRIAL_MEMBRANE}
SUBSTRATE: acyl Coenzyme A {CYTOPLASM.1134}
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
PRODUCT: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {CYTOPLASM.1134}
14) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
15) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
16) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
17) ==> enzymatic reaction
ENZYME: carnitine palmitoyl transferase-2
SUBSTRATE: acylcarnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}
coenzyme A {MITOCHONDRIAL_MATRIX.2612}
PRODUCT: acyl Coenzyme A
carnitine {INNER_MITOCHONDRIAL_MEMBRANE.3547}