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telangiectasia macularis eruptiva perstans (TMEP)
A generalized cutaneous mastocytosis.
Clinical manifestations:
1) freckle-like macules with fine telangiectasia in a chronic lesion
2) positive Darier's sign
3) dermatographism
4) hundreds of lesions
5) centripedal distribution, trunk > extremities
6) lesions may be confluent
Differential diagnosis:
1) Histiocytosis
2) secondary syphilis
3) sarcoid
4) histiocytoma
5) non-X histiocytosis
Related
Darier's sign
dermatographism
General
mastocytosis
References
- Color Atlas & Synopsis of Clinical Dermatology, Common
& Serious Diseases, 3rd ed, Fitzpatrick et al, McGraw Hill, NY,
1997, pg 718, 562-65
- Costa DL1, Moura HH, Rodrigues R et al
Telangiectasia Macularis Eruptiva Perstans
J Clin Aesthet Dermatol. Oct 2011; 4(10): 52-54
PMID: 22010057