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squalene synthetase (farnesyl-diphosphate farnesyltransferase, FDFT1, SQS)

Function: - steroid biosynthesis - terpenoid biosynthesis 2 farnesyl diphosphate diphosphate + presqualene diphosphate presqualene diphosphate + NADH/NADPH squalene + diphosphate + NAD+/NADP+ Cofactor: Mg+2 Structure: - monomer (putative) - belongs to the phytoene/squalene synthetase family Compartment: - endoplasmic reticulum membrane

Interactions

molecular events

Related

cholesterol biosynthesis squalene synthetase gene

General

membrane protein oxidoreductase prenyltransferase

Properties

SIZE: entity length = 417 aa MW = 48 kD COMPARTMENT: smooth endoplasmic reticulum MOTIF: cofactor-binding site COFACTOR-BOUND: NADPH transmembrane domain {284-304} transmembrane domain {384-404} SUBUNITS: prenyl transferase-alpha MOTIF: proline-rich region SITE: 22-31 MOTIF: proline residue (SEVERAL) PFTA {112-146} PFTA {147-180} PFTA {181-215} PFTA {216-249} PFTA {255-289} prenyl transferase-beta MOTIF: binding site FOR-BINDING-OF: ras superfamily protein GENE: squalene synthetase gene

Database Correlations

OMIM 184420 UniProt P37268 Entrez Gene 2222 ENZYME 2.5.1.21

References

UniProt :accession P37268

Components

CAAX farnesyltransferase alpha subunit (FNTA, RAS proteins prenyltransferase-alpha) prenyltransferase-beta