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sclerosing mesenteritis
Epidemiology: rare
Pathology:
- inflammation & fibrosis of the small intestine
Radiology:
- computed tomography (CT) of abdomen
- calcification in the mesentery is present in sclerosing mesenteritis but usually not other disorders
Differential diagnosis:
- lymphoma, carcinoid, desmoid tumors
Management:
- observation in mild cases
- tamoxifen (Soltamox) indefinitely plus prednisone tapered over 3 months
- surgery for intestinal obstruction
- follow surgery with tamoxifen & prednisone
General
intestinal disease
inflammation
sclerosis
References
- Mayo Clinic: Sclerosing Mesenteritis
http://www.mayoclinic.org/sclerosing-mesenteritis/
- Office of Rare Diseases Research (ORDR)
Sclerosing mesenteritis
http://rarediseases.info.nih.gov/GARD/Condition/8169/Sclerosing_mesenteritis.aspx