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sal-like protein 4; zinc finger protein SALL4 (SALL4)

Function: - probable transcription factor - interacts with NANOG (putative) Structure: - belongs to the sal C2H2-type Zn+2-finger protein family - contains 7 C2H2-type Zn+2 fingers Compartment: nucleus (probable) Expression: expressed in testis Pathology: - defects in SALL4 are the cause of a) Duane-radial ray syndrome b) IVIC syndrome

General

C2H2 type zinc finger protein nuclear protein

Properties

SIZE: entity length = 1053 aa MW = 112 kD COMPARTMENT: cell nucleus MOTIF: Zn finger C2H2-type SITE: 382-404 EFFECTOR-BOUND: Zn+2 Zn finger C2H2-type SITE: 410-432 EFFECTOR-BOUND: Zn+2 Zn finger C2H2-type SITE: 566-588 EFFECTOR-BOUND: Zn+2 Zn finger C2H2-type SITE: 594-616 EFFECTOR-BOUND: Zn+2 Zn finger C2H2-type SITE: 626-648 EFFECTOR-BOUND: Zn+2 Zn finger C2H2-type SITE: 870-892 EFFECTOR-BOUND: Zn+2 Zn finger C2H2-type SITE: 898-920 EFFECTOR-BOUND: Zn+2

Database Correlations

OMIM correlations MORBIDMAP 607343 UniProt Q9UJQ4 Pfam PF00096 Entrez Gene 57167 Kegg hsa:57167

References

  1. UniProt :accession Q9UJQ4
  2. GeneReviews http://www.ncbi.nlm.nih.gov/sites/genetests/lab/gene/SALL4