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pulmonary infiltrates with eosinophilia (PIE) syndrome
A group of heterogenous disorders characterized by the presence of abnormalities on chest X-ray & eosinophilia.
Etiology:
1) asthma
2) pulmonary eosinophilia
3) allergic bronchopulmonary aspergillosis
4) eosinophilic pneumonia
a) acute eosinophilic pneumonia
b) chronic eosinophilic pneumonia
5) Churg-Strauss disease
6) parasitic infections
- Loffler syndrome
7) pharmaceutical agents
8) neoplasms associated with eosinophilia:
a) eosinophilic leukemia
b) adenocarcinoma of the lung
c) lymphoma
9) tropical eosinophilia
10) hypereosinophilic syndrome
11) bronchocentric granulomatosis
Epidemiology:
- travel to developing country
Clinical manifestations:
- low grade fever
- dry cough
- wheezing
Laboratory:
- stool for ova & parasites
Radiology:
- patchy bilateral pulmonary infiltrates
Management:
- long-term systemic glucocorticoids
- case of symptoms & radiology findings clearing with 5 days of prednisone [2]
Related
eosinophilia
parasites frequently associated with eosinophilia
Specific
acute eosinophilic leukemia
allergic angiitis & granulomatosis of Churg-Strauss; eosinophilic granulomatosis with polyangiitis (EGPA)
allergic bronchopulmonary aspergillosis; allergic bronchopulmonary mycosis (ABPA)
bronchocentric granulomatosis
drugs causing eosinophilia
eosinophilic asthma
eosinophilic pneumonia; Andrews syndrome; pulmonary eosinophilia
hypereosinophilic syndrome
Loffler's syndrome (simple pulmonary eosinophilia)
tropical eosinophilia
General
pulmonary infiltrate
pulmonary esosinophilia
syndrome
References
- Mayo Internal Medicine Board Review, 1998-99, Prakash UBS (ed)
Lippincott-Raven, Philadelphia, 1998, pg 753
- NEJM Knowledge+ Complex Medical Care