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Procollagen galactosyltransferase 2; collagen beta(1-O)galactosyltransferase 2; glycosyltransferase 25 family member 2; hydroxylysine galactosyltransferase 2 (COLGALT2, C1orf17, GLT25D2, KIAA0584)
Function:
- has a beta-galactosyltransferase activity
- transfers beta-galactose to hydroxylysine residues on collagen
UDP-alpha-D-galactose + 5-hydroxy-L-lysine-[procollagen] =
UDP + 5-(D-galactosyloxy)-L-lysine-[procollagen]
Kinetic parameters:
- KM=33.5 uM for UDP-galactose
Structure:
- belongs to the glycosyltransferase 25 family
Compartment:
- endoplasmic reticulum lumen (putative)
Expression:
- expressed in brain & skeletal muscle
Note:
- has no glucosyltransferase activity
General
glycoprotein
Properties
SIZE: entity length = 626 aa
MW = 73 kD
COMPARTMENT: endoplasmic reticulum
MOTIF: signal sequence {1-27}
N-glycosylation site {N97}
N-glycosylation site {N185}
N-glycosylation site {N382}
N-glycosylation site {N580}
Prevents secretion from ER {623-626}
Database Correlations
UniProt Q8IYK4
Pfam PF01755
Entrez Gene 23127
Kegg hsa:23127
ENZYME 2.4.1.50
References
UniProt :accession Q8IYK4