Specific

3-beta hydroxy-5-ene steroid dehydrogenase type 1; steroid delta isomerase; progesterone reductase (HSD3B1, HSDB3A) acyl CoA dehydrogenase acylglycerol kinase mitochondrial ADP/ATP translocase 4 (adenine nucleotide translocator 4, ANT 4, ADP,ATP carrier protein 4, sperm flagellar energy carrier protein, solute carrier family 25 member 31, SLC25A31, AAC4, ANT4, SFEC) ADP/ATP translocase, adenine nucleotide translocase (ANT) or ADP/ATP carrier protein adrenodoxin reductase (ferredoxin NADP reductase, FDXR) AFG3-like protein 2 (paraplegin-like protein, AFG3L2) aspartate/glutamate translocase or aspartate/glutamate carrier protein ATP synthase B chain; F0 b element; coupling factor 0-b (ATP5F1) ATP synthase D chain (ATP5H) ATP synthase E chain (ATP5I) ATP synthase F chain (ATP5J2, ATP5JL) ATP synthase G chain (ATP5L) ATP synthase subunit g2, mitochondrial (ATPase subunit g2, ATP5L2, ATP5K2) B-cell leukemia-2 (bcl-2) protein branched-chain ketoacid dehydrogenase Ca+2 uptake protein 1, mitochondrial; atopy-related autoantigen CALC; ara CALC; Ca+2-binding atopy-related autoantigen 1; allergen hom s 4 (MICU1 CALC CBARA1) carnitine O-palmitoyltransferase 1 (carnitine palmitoyltransferase 1C, CPT 1C, CPT1C) carnitine palmitoyltransferase coiled-coil domain-containing protein 90B, mitochondrial (CCDC90B) coupling factor 0 (F0, CF0) COX16-like protein C14orf112, mitochondrial (COX16) cytochrome a cytochrome a3 cytochrome b (ubiquinol-cytochrome-c reductase complex cytochrome b subunit, cytochrome b-c1 complex subunit 3, complex 3 subunit 3, MT-CYB, COB, CYTB, MTCYB) cytochrome b-c1 complex subunit 1, mitochondrial; complex III subunit 1; core protein I; ubiquinol-cytochrome-c reductase complex core protein 1; process-enhancing protein (UQCRC1) cytochrome b-c1 complex subunit 10; complex III subunit 10; complex III subunit XI; ubiquinol-cytochrome c reductase complex 6.4 kD protein (UQCR11, UQCR) cytochrome b-c1 complex subunit 2, mitochondrial; complex III subunit 2; core protein 2; ubiquinol-cytochrome-c reductase complex core protein 2 (UQCRC2) cytochrome b-c1 complex subunit 6, mitochondrial; complex III subunit 6; complex III subunit VI; cytochrome c1 non-heme 11 kD protein; mitochondrial hinge protein; ubiquinol-cytochrome c reductase complex 11 kD protein (UQCRH) cytochrome b-c1 complex subunit 7; complex III subunit 7; complex III subunit VII; QP-C; ubiquinol-cytochrome c reductase complex 14 kD protein (UQCRB, UQBP) cytochrome b-c1 complex subunit 8; complex III subunit 8; complex III subunit VIII; ubiquinol-cytochrome c reductase complex 9.5 kD protein; ubiquinol-cytochrome c reductase complex ubiquinone-binding protein QP-C (UQCRQ) cytochrome b-c1 complex subunit 9; complex III subunit 9; complex III subunit X; cytochrome c1 non-heme 7 kD protein; ubiquinol-cytochrome c reductase complex 7.2 kD protein (UQCR10, UCRC, HSPC119) cytochrome b-c1 complex subunit Rieske, mitochondrial; complex III subunit 5; cytochrome b-c1 complex subunit 5; Rieske iron-sulfur protein; RISP; ubiquinol-cytochrome c reductase iron-sulfur subunit; contains: cytochrome b-c1 complex subunit 11; complex III subunit IX; ubiquinol-cytochrome c reductase 8 kD protein (UQCRFS1) cytochrome b5 type B; cytochrome b5 outer mitochondrial membrane isoform (CYB5B, CYB5M, OMB5) cytochrome c oxidase (complex IV) cytochrome c oxidase assembly protein COX11, mitochondrial (COX11) cytochrome c oxidase assembly protein COX15 homolog (COX15) cytochrome c oxidase subunit 1; cytochrome c oxidase polypeptide I (MT-CO1 COI COXI MTCO1) cytochrome c oxidase subunit 7A-related protein, mitochondrial; cytochrome c oxidase subunit VIIa-related protein; COX7a-related protein; EB1 (COX7A2L, COX7AR, COX7RP) cytochrome P450 11A1 (CYP11A1, cholesterol 20,22 desmolase, cytochrome P450 SCC, CYP11A1) cytochrome P450 11B (steroid-11-beta hydroxylase) Death-inducing protein (DIP, GRAMD4, KIAA0767) dicarboxylate carrier or malate transporter E3 ubiquitin-protein ligase MARCH5 (membrane-associated RING finger protein 5, membrane-associated RING-CH protein V, MARCH-5, RING finger protein 153, MARCH5, RNF153) electrogenic H+ ATPase or proton pump electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial; ETF-ubiquinone oxidoreductase; ETF-QO; electron-transferring-flavoprotein dehydrogenase; ETF dehydrogenase (ETFDH) glycerol-3-phosphate acyltransferase, mitochondrial (GPAT, GPAM, KIAA1560) hepatocellular carcinoma-down-regulated mitochondrial carrier protein; solute carrier family 25 member 47 (SLC25A47, C14orf68, HDMCP, HMFN1655) hexaprenyl pyrophosphate synthetase Hexokinase-1 (hexokinase type I, HK I, brain form hexokinase, HK1) hexokinase-2 (hexokinase type II, HK II, muscle form hexokinase, HK2) hydroxyacyl-coenzyme A dehydrogenase, mitochondrial; HCDH; medium & short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase; short-chain 3-hydroxyacyl-CoA dehydrogenase (HADH, HAD, HADHSC, SCHAD) Inner membrane protein COX18, mitochondrial precursor (cytochrome c oxidase assembly protein 18, COX18Hs, COX18, OXA1L2) ISP42 ISP6 kidney mitochondrial carrier protein 1 (solute carrier family 25 member 30, SLC25A30, KMCP1) kynurenine 3-monooxygenase; kynurenine 3-hydroxylase (KMO) leucine zipper-EF-hand-containing transmembrane protein 1 (LETM1) MAS20 MAS20/MAS22 subcomplex MAS22 MAS37 MAS70 MAS70/MAS37 subcomplex Mg+2 transporter MRS2L, mitochondrial (MRS2-like protein, MRS2L, HPT, MRS2) mitochondrial 2-oxoglutarate/malate carrier protein; OGCP; solute carrier family 25 member 11 (SLC25A11 SLC20A4) mitochondrial antiviral-signaling protein; MAVS; CARD adapter inducing interferon beta; cardif; interferon beta promoter stimulator protein 1; IPS-1; NF-kappa-B-activating protein 031N; virus-induced-signaling adapter; VISA (MAVS, IPS1, KIAA1271, VISA) mitochondrial Ca+2 uniporter regulator 1; coiled-coil domain-containing protein 90A, mitochondrial (MCUR1 C6orf79, CCDC90A) mitochondrial carnitine/acylcarnitine carrier protein CACL; CACT-like; solute carrier family 25 member 29 (SLC25A29, C14orf69) mitochondrial carrier homolog 1 (presenilin-associated protein, MTCH1, PSAP, UNQ1871/PRO4314) mitochondrial carrier homolog 2 (Met-induced mitochondrial protein, MTCH2, MIMP, HSPC032) mitochondrial carrier triple repeat protein 1; solute carrier family 25 member 51 (MCART1, SLC25A51) mitochondrial carrier triple repeat protein 2; solute carrier family 25 member 52 (MCART2, SLC25A52) mitochondrial carrier triple repeat protein 6; solute carrier family 25 member 53 (MCART6, SLC25A53) mitochondrial chaperone BCS1; h-BCS1; BCS1-like protein (BCS1L BCS1) mitochondrial dynamic protein MID49; mitochondrial dynamic protein of 49 kDa; mitochondrial elongation factor 2; Smith-Magenis syndrome chromosomal region candidate gene 7 protein (MIEF2 MID49 SMCR7) mitochondrial dynamic protein MID51; mitochondrial dynamic protein of 51 kD; mitochondrial elongation factor 1; Smith-Magenis syndrome chromosomal region candidate gene 7 protein-like (MIEF1, MID51, SMCR7L) mitochondrial fission regulator 1; chondrocyte protein with a poly-proline region (MTFR1, CHPPR, KIAA0009) mitochondrial glutamate carrier 1 (GC-1, glutamate/H+ symporter 1, solute carrier family 25 member 22, SLC25A22, GC1) mitochondrial import inner membrane translocase subunit (TIM, translocase of inner mitochondrial membrane, mitochondrial protein importer) mitochondrial import inner membrane translocase subunit TIM10 (TIMM10 ,TIM10) mitochondrial import inner membrane translocase subunit TIM13 (TIMM13, TIM13B, TIMM13A, TIMM13B) mitochondrial import inner membrane translocase subunit TIM14 (DnaJ homolog subfamily C member 19, DNAJC19, TIM14, TIMM14) mitochondrial import inner membrane translocase subunit TIM17A (TIMM17A, MIMT17, TIM17, TIM17A, TIMM17) mitochondrial import inner membrane translocase subunit TIM17B (TIMM17B, TIM17B, JM3) mitochondrial import inner membrane translocase subunit TIM22 (testis-expressed sequence 4, TIMM22, TEX4, TIM22) mitochondrial import inner membrane translocase subunit TIM23 (TIMM23, TIM23) mitochondrial import inner membrane translocase subunit TIM44 (TIMM44, MIMT44, TIM44) mitochondrial import inner membrane translocase subunit TIM50 (TIMM50, TIM50, PRO1512) mitochondrial import inner membrane translocase subunit TIM8A; deafness dystonia protein 1; X-linked deafness dystonia protein (TIMM8A, DDP, DDP1, TIM8A) mitochondrial import inner membrane translocase subunit TIM8B; deafness dystonia protein 2; DDP-like protein (TIMM8B, TIM8B) mitochondrial import inner membrane translocase subunit TIM9A (TIMM9, TIM9, TIM9A, TIMM9A) mitochondrial import inner membrane translocase subunit TIM9B (fracture callus protein 1, FxC1, TIM10B) mitochondrial import receptor subunit TOM20 homolog; mitochondrial 20 kD outer membrane protein; outer mitochondrial membrane receptor Tom20 (TOMM20, KIAA0016) mitochondrial import receptor subunit TOM22 homolog; translocase of outer membrane 22 kD subunit homolog (TOMM22, TOM22, hTom22, 1C9-2) mitochondrial import receptor subunit TOM34 homolog; translocase of outer membrane 34 kD subunit (TOMM34, URCC3) mitochondrial import receptor subunit TOM40 homolog; protein Haymaker; translocase of outer membrane 40 kD subunit homolog; p38.5 (TOMM40, C19orf1, PEREC1, TOM40) mitochondrial import receptor subunit TOM6 homolog; overexpressed breast tumor protein; translocase of outer membrane 6 kD subunit homolog (TOMM6, OBTP, TOM6) mitochondrial import receptor subunit TOM7 homolog; translocase of outer membrane 7 kD subunit homolog (TOMM7, TOM7, TOMM07, AD-014) mitochondrial inner membrane protease mitochondrial inner membrane protease subunit 1 (IMP1-like protein, IMMP1L) mitochondrial inner membrane protease subunit 2 (IMP2-like protein, IMMP2L) mitochondrial inner membrane protein OXA1L; Hsa; OXA1Hs; oxidase assembly 1-like protein; OXA1-like protein (OXA1L) mitochondrial receptor complex; preprotein translocase complex; TOM complex mitochondrial Rho GTPase 1 (MIRO-1, hMiro-1, Ras homolog gene family member T1, Rac-GTP-binding protein-like protein, RHOT1, ARHT1) mitochondrial Rho GTPase 2 (MIRO-2, hMiro-2, Ras homolog gene family member T2, RHOT2, ARHT2, C16orf39) mitochondrial ribosome-associated GTPase 2; GTP-binding protein 5; protein obg homolog 1; ObgH1 (MTG2, GTPBP5, OBGH1) mitochondrial-processing peptidase mitoferrin-1 (mitochondrial iron transporter 1, solute carrier family 25 member 37, mitochondrial solute carrier protein, SLC25A37, MFRN, MSCP, HT015) mitoferrin-2 (mitochondrial iron transporter 2, solute carrier family 25 member 28, mitochondrial RNA splicing protein 3/4 homolog, MRS3/4, hMRS3/4 , SLC25A28, MFRN2, NPD016) mitofilin (mitochondrial inner membrane protein, p87/89, proliferation-inducing gene 4 protein, IMMT, HMP, PIG4) monoamine oxidase (MAO) Na+/H+ exchanger NHE6 (solute carrier family 9 isoform 6, SLC9A6) NADP+ transhydrogenase mitochondrial; pyridine nucleotide transhydrogenase, nicotinamide nucleotide transhydrogenase (NNT) PAM complex paraplegin; spastic paraplegia 7 protein (SPG7, CAR, CMAR, PGN) phosphate carrier (phosphate transporter/translocase, PTP, solute carrier family 25 member 3, SLC25A3, PHC, OK/SW-cl48) Presenilins-associated rhomboid-like protein, mitochondrial prohibitin-2; B-cell receptor-associated protein BAP37; repressor of estrogen receptor activity; D-prohibitin (PHB2, REA, BAP) protein Mpv17; glomerulosclerosis protein MPV17, human homolog (MPV17) protein spinster homolog 1 (spinster-like protein 1, HSpin1, SPNS1, SPIN1, PP20300) protein TOMM40-like (TOMM40L) regulator of microtubule dynamics protein 3; RMD-3; hRMD-3; cerebral protein 10; protein FAM82A2; protein FAM82C; protein tyrosine phosphatase-interacting protein 51; TCPTP-interacting protein 51 (RMDN3, FAM82A2, FAM82C, PTPIP51, hucep-10, UNQ3122/PRO10274) sarcomeric/mitochondrial creatine kinase (S-mtCK, CKMT2) serine protease HTRA2, mitochondrial; high temperature requirement protein A2; HtrA2; Omi stress-regulated endoprotease; serine protease 25; serine proteinase OMI (HTRA2, OMI, PRSS25) serine/threonine protein kinase PINK1, mitochondrial; PTEN-induced putative kinase protein 1; BRPK (PINK1) sideroflexin-1; tricarboxylate carrier protein; TCC (SFXN1) sideroflexin-2 (SFXN2) sideroflexin-3 (SFXN3) single-pass membrane protein with aspartate-rich tail 1, mitochondrial (SMDT1, C22orf32) solute carrier family 25 member 13; Ca+2-binding mitochondrial carrier protein Aralar2; citrin; mitochondrial aspartate glutamate carrier 2 (SLC25A13, ARALAR2) solute carrier family 25 member 15; mitochondrial ornithine transporter 1 (SLC25A15, ORNT1, SP1855) solute carrier family 25 member 18; mitochondrial glutamate carrier 2; GC-2; glutamate/H+ symporter 2 (SLC25A18, GC2) solute carrier family 25 member 19; mitochondrial thiamine pyrophosphate carrier; mitochondrial uncoupling protein 1 (SLC25A19, DNC, MUP1) solute carrier family 25 member 2 (SLC25A2, mitochondrial ornithine transporter 2, ORNT2) solute carrier family 25 member 21; mitochondrial 2-oxodicarboxylate carrier (SLC25A21, ODC) solute carrier family 25 member 32 (SLC25A39, mitochondrial folate transporter/carrier, MFT, MFTC) solute carrier family 25 member 33 (bone marrow stromal cell mitochondrial carrier protein, BMSC-MCP, HuBMSC-MCP, protein PNC1, SLC25A33) solute carrier family 25 member 34 (SLC25A34) solute carrier family 25 member 35 (SLC25A35) solute carrier family 25 member 36 (SLC25A36) solute carrier family 25 member 38 (SLC25A38) solute carrier family 25 member 39 (SLC25A39) solute carrier family 25 member 40 (mitochondrial carrier family protein, SLC25A40, MCFP) solute carrier family 25 member 42 (SLC25A42) solute carrier family 25 member 43 (SLC25A43) solute carrier family 25 member 44 (SLC25A44, KIAA0446) solute carrier family 25 member 45 (SLC25A45) solute carrier family 25 member 46 (SLC25A46, TB1) solute carrier family 25 member 48; mitochondrial carrier protein FLJ44862 (SLC25A48) sorting & assembly machinery component 50 homolog (SAMM50) spermatogenesis-associated protein 19, mitochondrial (spermatogenic cell-specific gene 1 protein, spergen-1, SPATA19, SPERGEN1) steroidogenic acute regulatory protein, mitochondrial; StAR; StARD1 (STAR) succinate dehydrogenase cytochrome b small subunit (cybS, succinate dehydrogenase complex subunit D, SDHD) succinate dehydrogenase cytochrome b560 subunit (succinate dehydrogenase complex subunit C, succinate-ubiquinone oxidoreductase cytochrome B large subunit, CYBL, SDHC, CYB560, SDH3) succinate dehydrogenase flavoprotein subunit (SDHA, SDH2, SDHF) synaptojanin-2-binding protein (mitochondrial outer membrane protein 25, SYNJ2BP, OMP25) tetratricopeptide repeat protein 11; mitochondrial fission 1 protein; FIS1 homolog; hFis1; tetratricopeptide repeat protein 11; TPR repeat protein 11 (FIS1, TTC11, CGI-135) TIM21-like protein, mitochondrial (TIMM21, C18orf55) Translocase of outer membrane TOM70 (mitochondrial precursor proteins import receptor, TOMM70A, KIAA0719) translocator protein; peripheral-type benzodiazepine receptor; PBR; PKBS; mitochondrial benzodiazepine receptor (TSPO, BZRP, MBR) transmembrane GTPase MFN1; mitofusin-1; Fzo homolog (MFN1) transmembrane GTPase MFN2l mitofusin-2 (MFN2, CPRP1, KIAA0214) tricarboxylate transport protein, mitochondrial; citrate transport protein; CTP; tricarboxylate carrier protein; solute carrier family 25 member 1 (SLC25A1, SLC20A3) ubiquinol cytochrome c reductase; respiratory complex 3 ubiquinone biosynthesis protein COQ4 homolog, mitochondrial; coenzyme Q biosynthesis protein 4 homolog (COQ4) ubiquitin carboxyl-terminal hydrolase 30; deubiquitinating enzyme 30; ubiquitin thiolesterase 30; ubiquitin-specific-processing protease 30; Ub-specific protease 30 (USP30) uncoupling protein very long-chain specific acyl-CoA dehydrogenase, mitochondrial; VLCAD (ACADVL, VLCAD) voltage-dependent anion-selective channel protein 1; VDAC-1; hVDAC1; outer mitochondrial membrane protein porin 1; plasmalemmal porin; porin 31HL; porin 31HM (VDAC1 VDAC) voltage-dependent anion-selective channel protein 2; VDAC-2; hVDAC2; outer mitochondrial membrane protein porin 2 (VDAC2) voltage-dependent anion-selective channel protein 3; VDAC-3; hVDAC3; outer mitochondrial membrane protein porin 3 (VDAC3) yeast mitochondrial protein import channel yeast mitochondrial protein importer

General

membrane protein mitochondrial protein