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lysyl oxidase homolog 4 (lysyl oxidase-like protein 4, lysyl oxidase-related protein C, LOXL4, LOXC)

Function: - modulates formation of collagenous extracellular matrix (putative) , Cofactor: Cu+, Cu+2 Structure: - belongs to the lysyl oxidase family - contains 4 SRCR domains - contains 1 lysine tyrosylquinone, generated by condensation of epsilon-amino group of Lys with topaquinone produced by oxidation of Tyr Compartment: secreted Expression: - expressed in many tissues - highest levels in skeletal muscle, testis, pancreas - expressed in cartilage

General

glycoprotein metalloprotein oxidoreductase secreted protein

Properties

SIZE: MW = 84 kD entity length = 756 aa COMPARTMENT: extracellular compartment MOTIF: signal sequence {1-24} SRCR 1 {32-133} MOTIF: cysteine residue {C58} MODIFICATION: cysteine residue {C122} cysteine residue {C71} MODIFICATION: cysteine residue {C132} cysteine residue {C102} MODIFICATION: cysteine residue {C112} cysteine residue {C112} MODIFICATION: cysteine residue {C102} cysteine residue {C122} MODIFICATION: cysteine residue {C58} cysteine residue {C132} MODIFICATION: cysteine residue {C71} SRCR 2 {159-287} MOTIF: cysteine residue {C191} MODIFICATION: cysteine residue {C276} N-glycosylation site {N198} cysteine residue {C204} MODIFICATION: cysteine residue {C286} cysteine residue {C251} MODIFICATION: cysteine residue {C261} cysteine residue {C261} MODIFICATION: cysteine residue {C251} cysteine residue {C276} MODIFICATION: cysteine residue {C191} cysteine residue {C286} MODIFICATION: cysteine residue {C204} SRCR 3 {311-411} MOTIF: cysteine residue {C336} MODIFICATION: cysteine residue {C400} cysteine residue {C349} MODIFICATION: cysteine residue {C410} cysteine residue {C380} MODIFICATION: cysteine residue {C390} cysteine residue {C390} MODIFICATION: cysteine residue {C380} cysteine residue {C400} MODIFICATION: cysteine residue {C336} cysteine residue {C410} MODIFICATION: cysteine residue {C349} SRCR 4 {421-529} MOTIF: cysteine residue {C450} MODIFICATION: cysteine residue {C515} cysteine residue {C463} MODIFICATION: cysteine residue {C528} cysteine residue {C497} MODIFICATION: cysteine residue {C507} cysteine residue {C507} MODIFICATION: cysteine residue {C497} cysteine residue {C515} MODIFICATION: cysteine residue {C450} cysteine residue {C528} MODIFICATION: cysteine residue {C463} Lysyl-oxidase like {533-736} MOTIF: copper [Cu]-binding site SITE: 611-611 MOTIF: histidine residue (3) copper [Cu]-binding site SITE: 613-613 MOTIF: histidine residue (3) copper [Cu]-binding site SITE: 615-615 MOTIF: histidine residue (3) N-glycosylation site {N629}

Database Correlations

OMIM 607318 UniProt Q96JB6 PFAM correlations

References

UniProt :accession Q96JB6