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Interactions
molecular events
Specific
alpha-galactosidase or galactoside galactohydrolase
arylsulfatase-A (cerebroside sulfatase, [contains: arylsulfatase A component B; arylsulfatase A component C], ARSA)
arylsulfatase-B (ARSB, chondro-4-sulfatase, N-acetylgalactosamine-4-sulfatase)
arylsulfatase-D (ARSD)
aspartylglucosaminidase (N-aspartyl-beta-glucosaminidase, N4-(beta-N-acetylglucosaminyl)-L-asparaginase, glycosylasparaginase, [contains: glycosylasparaginase alpha chain; glycosylasparaginase beta chain], AGA)
beta glucuronidase (GUSB, beta-G1, MPS7)
cathepsin
iduronate-2-sulfatase (IDS, alpha-L-iduronate sulfate sulfatase)
lysosomal acid lipase; cholesterol ester hydrolase
lysosomal acid phosphatase (LAP)
lysosomal alpha-glucosidase; alpha-1,4-glucosidase; acid alpha glucosidase; acid maltase (GAA)
lysosomal DNase
muramidase or lysozyme
sphingomyelinase, sphinogomyelin phosphodiesterase
General
glycoprotein
hydrolase