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hydroxyacid oxidase 2; (S)-2-hydroxy-acid oxidase, peroxisomal; long chain alpha-hydroxy acid oxidase; long-chain L-2-hydroxy acid oxidase (HAOX2, HAO2)
Function:
1) catalyzes oxidation of L-alpha-hydroxy acids & more slowly, oxidation of L-alpha-amino acids.
(S)-2-hydroxy acid + O2 2-oxo acid + H2O2
Cofactor: FMN
Compartment: peroxisome
Expression: expressed in liver & kidney
Related
glycolate
General
flavoprotein
oxidoreductase
Properties
SIZE: MW = 39 kD
entity length = 351 aa
MOTIF: histidine residue {H246}
microbody-targeting signal {349-351}
Database Correlations
OMIM 605176
UniProt Q9NYQ3
Pfam PF01070
ENZYME 1.1.3.15
References
UniProt :accession Q9NYQ3