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glycogen phosphorylase

Function: - allosteric enzyme in carbohydrate metabolism - catalyzes formation of glucose-1-phosphate from glycogen during glycogenolysis - enzymes from different sources differ in their regulatory mechanisms & in their natural substrates - all known phosphorylases share catalytic & structural properties - activity of phosphorylase is controlled both by allosteric means (through the noncovalent binding of metabolites) & by covalent modification - AMP allosterically activates, whereas ATP, ADP, & glucose-6-phosphate allosterically inhibit - phosphorylation by phosphorylase kinase activates (1,4-alpha-D-glucosyl)(n)* + phosphate (1,4-alpha-D-glucosyl)(n-1)* + alpha-D glucose-1-phosphate * glycogen Cofactor: pyridoxal phosphate Pathology: - defects associated with glycogen storage disease type V (McArdle Disease) Laboratory: - phosphorylase in erythrocytes

Interactions

molecular events

Specific

phosphorylase-A phosphorylase-B (brain glycogen phosphorylase, PYGB) phosphorylase-L (liver glycogen phosphorylase, PYGL) phosphorylase-M (myophosphorylase, muscle glycogen phosphorylase, PYGM)

General

hexosyltransferase oligomerizing protein phosphoprotein phosphotransferase regulatory molecule

Properties

CONFIGURATION: dimer SIZE: MW = 97 kD COMPARTMENT: cytoplasm MOTIF: Ser phosphorylation site {S14} kinase domain MOTIF: ATP-binding site NAME: ATP-binding site cofactor-binding site COFACTOR-BOUND: pyridoxal phosphate

Database Correlations

ENZYME 2.4.1.1

References

  1. Textbook of Biochemistry with Clinical Correlations, 3rd ed., TM Devlin (ed), Wiley-Liss, NY 1992 pg 346
  2. Wikipedia: Glycogen phosphorylase https://en.wikipedia.org/wiki/Glycogen_phosphorylase