extracellular matrix protein 1 (secretory component p85, ECM1)

Compartment: secreted Pathology: - defects in ECM1 are the cause of lipoid proteinosis

General

glycoprotein secreted protein

Properties

SIZE: MW = 61 kD entity length = 540 aa COMPARTMENT: extracellular compartment MOTIF: signal sequence {1-19} 2 X approximate repeats {150-405} MOTIF: consensus repeat {150-279} consensus repeat {283-405} N-glycosylation site {N354} N-glycosylation site {N444} N-glycosylation site {N530}

Database Correlations

OMIM correlations MORBIDMAP 602201 UniProt Q16610 Pfam PF05782

References

UniProt :accession Q16610