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steroid hormone receptor ERR2; estrogen-related receptor, beta; ERR-beta; estrogen receptor-like 2; ERR beta-2; nuclear receptor subfamily 3 group B member 2 (ESRRB, ERRB2, ESRL2, NR3B2)

Structure: - homodimer (putative) - belongs to the nuclear hormone receptor family, NR3 subfamily - contains 1 nuclear receptor DNA-binding domain Compartment: nucleus (putative) Pathology: - defects in ESRRB are the cause of autosomal recessive non-syndromic sensorineural deafness type 35

General

receptor steroid receptor zinc finger protein

Properties

SIZE: entity length = 500 aa MW = 56 kD COMPARTMENT: cell nucleus MOTIF: DNA-binding motif SITE: 100-175 MOTIF: Zn finger C4-type SITE: 103-123 EFFECTOR-BOUND: Zn+2 Zn finger C4-type SITE: 139-163 EFFECTOR-BOUND: Zn+2

Database Correlations

OMIM correlations MORBIDMAP 602167 UniProt O95718 PFAM correlations Kegg hsa:2103

References

UniProt :accession O95718