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epidermolysis bullosa

Management: 1) mild forms may not require extensive treatment a) keep blisters from forming b) prevent infection when blisters occur 2) moderate and severe forms a) may have many complications b) may require psychological support c) attention to the care & protection of the skin & soft tissues 3) treat infection 4) surgery may be indicated 3) multidisciplinary team approach -> physicians, nurses, social workers, clergy members, psychologists, dietitians 4) patient & parent support groups

Specific

epidermolysis bullosa acquisita (EBA) epidermolysis bullosa aquisita epidermolysis bullosa dystrophica (EBD) epidermolysis bullosa lethal acantholytic (EBLA) epidermolysis bullosa simplex (EBS) epidermolysis bullosa with pyloric atresia; aplasia cutis congenita with gastrointestinal atresia epidermolysis bullosa, junctional

General

chronic skin disease (chronic dermatologic disorder, chronic dermatopathy, chronic dermatosis) epidermolytic disorder

References

Epidermolysis Bullosa https://www.niams.nih.gov/health-topics/epidermolysis-bullosa