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epidermolysis bullosa
Management:
1) mild forms may not require extensive treatment
a) keep blisters from forming
b) prevent infection when blisters occur
2) moderate and severe forms
a) may have many complications
b) may require psychological support
c) attention to the care & protection of the skin & soft tissues
3) treat infection
4) surgery may be indicated
3) multidisciplinary team approach
-> physicians, nurses, social workers, clergy members, psychologists, dietitians
4) patient & parent support groups
Specific
epidermolysis bullosa acquisita (EBA)
epidermolysis bullosa aquisita
epidermolysis bullosa dystrophica (EBD)
epidermolysis bullosa lethal acantholytic (EBLA)
epidermolysis bullosa simplex (EBS)
epidermolysis bullosa with pyloric atresia; aplasia cutis congenita with gastrointestinal atresia
epidermolysis bullosa, junctional
General
chronic skin disease (chronic dermatologic disorder, chronic dermatopathy, chronic dermatosis)
epidermolytic disorder
References
Epidermolysis Bullosa
https://www.niams.nih.gov/health-topics/epidermolysis-bullosa