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elastase-1; pancreatic elastase 1; chymotrypsin-like elastase family member 1 (ELA1, CELA1)

Function: - hydrolysis of proteins, including elastin - preferential cleavage: Ala-|-Xaa Cofactor: binds 1 Ca+2 per subunit (putative) Structure: - belongs to the peptidase S1 family, elastase subfamily - contains 1 peptidase S1 domain Compartment: secreted Expression: skin; not expressed in pancreas Laboratory: - pancreatic elastase in body fluid - pancreatic elastase in serum - pancreatic elastase free in serum - pancreatic elastase in stool

General

Ca+2 binding protein elastase glycoprotein

Properties

SIZE: entity length = 258 aa MW = 28 kD MOTIF: signal sequence {1-8} S1 domain {19-256} MOTIF: cysteine residue {C48} MODIFICATION: cysteine residue {C64} histidine residue {H63} cysteine residue {C64} MODIFICATION: cysteine residue {C48} Ca+2-binding site SITE: 77-77 N-glycosylation site {N79} Ca+2-binding site SITE: 82-82 Ca+2-binding site SITE: 87-87 aspartate residue {D111} cysteine residue {C145} MODIFICATION: cysteine residue {C212} cysteine residue {C176} MODIFICATION: cysteine residue {C192} cysteine residue {C192} MODIFICATION: cysteine residue {C176} cysteine residue {C202} MODIFICATION: cysteine residue {C232} serine residue {S206} cysteine residue {C212} MODIFICATION: cysteine residue {C145} cysteine residue {C232} MODIFICATION: cysteine residue {C202} N-glycosylation site {N233} MISC-INFO: INHIBITOR = ALPHA_1_PROTEASE_INHIBITOR

Database Correlations

OMIM 130120 UniProt Q9UNI1 Entrez Gene 1990 ENZYME 3.4.21.36

References

  1. OMIM :accession 130120 155250
  2. prosite :accession PS00134
  3. Wikipedia; Note=Elastase entry http://en.wikipedia.org/wiki/Elastase