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E3 ubiquitin-protein ligase HERC1 (HECT domain & RCC1-like domain-containing protein 1, p532, p619, HERC1)

Function: - role in membrane trafficking via some guanine nucleotide exchange factor (GEF) activity & its ability to bind clathrin - acts as a GEF for Arf & Rab, by exchanging bound GDP for free GTP - binds phosphatidylinositol-4,5-bisphosphate, which is required for GEF activity - may also act as a E3 ubiquitin-protein ligase - interacts with TSC2; interaction is inhibited by TSC1 - interacts with PKM2, ARF1 & ARF6 - forms a ternary complex with clathrin heavy chain (CLTC) & HSPA1A - protein degradation; protein ubiquitination - phosphorylated upon DNA damage, probably by ATM or ATR Structure: - contains 1 B30.2/SPRY domain - contains 1 HECT domain (E6AP-type E3 ubiquitin-protein ligase domain) - contains 14 RCC1 repeats - contains 11 WD repeats Compartment: - peripheral membrane - cytoplasm - Golgi - recruited onto actin-rich surface protrusions Expression: widely expressed

General

guanine nucleotide exchange factor (GDP/GTP dissociation stimulator, guanine nucleotide-releasing factor/protein, GNEF, GNDS, GDS) phosphoprotein E3 ubiquitin ligase; ubiquitin-ligating enzyme E3; N end-recognizing protein WD repeat protein family

Properties

SIZE: entity length = 4861 aa MW = 532 kD COMPARTMENT: cytoplasm golgi MOTIF: RCC1 repeat {371-420} RCC1 repeat {421-475} WD repeat {441-483} RCC1 repeat {476-528} WD repeat {506-545} RCC1 repeat {529-578} RCC1 repeat {580-631} RCC1 repeat {633-682} WD repeat {660-699} RCC1 repeat {683-735} glutamate-rich region {1349-1378} MOTIF: glutamate residue (SEVERAL) Ser phosphorylation site {S1514} Ser phosphorylation site {S1517} Ser phosphorylation site {S1521} B30.2/SPRY {2002-2193} WD repeat {3426-3465} WD repeat {3484-3522} WD repeat {3524-3572} WD repeat {3580-3619} WD repeat {3624-3663} MOTIF: Thr phosphorylation site {T3628} Ser phosphorylation site {S3631} Thr phosphorylation site {T3643} WD repeat {3667-3713} WD repeat {3745-3784} RCC1 repeat {3996-4044} RCC1 repeat {4046-4099} RCC1 repeat {4101-4151} RCC1 repeat {4153-4203} RCC1 repeat {4205-4256} RCC1 repeat {4258-4308} WD repeat {4287-4325} RCC1 repeat {4310-4360} HECT domain {4501-4848} MOTIF: Thr phosphorylation site {T4786} Ser phosphorylation site {S4790} cysteine residue {C4811}

Database Correlations

OMIM 605109 UniProt Q15751 PFAM correlations

References

UniProt :accession Q15751