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dermatologic manifestations of rheumatologic disease
Clinical manifestations:
1) systemic lupus erythematosus
a) malar rash
b) photosensitivity rash
c) discoid lupus
d) subacute cutaneous lupus erythematosus
e) oral mucocutaneous ulcerations
- on tongue or hard palate
- generally painless
f) alopecia
g) lupus panniculitis
2) dermatomyositis
a) Grotton's papules on extensor surfaces of metacarpophangeal joints & proximal interphalangeal joints
b) macular erythema
- shawl sign: rash involves posterior neck, upper back, & shoulders
- V sign: rash involves anterior neck & chest
c) heliotrope rash (violaceous rash on upper eyelid)
d) dry, cracked fingers & hands
e) nailfold capillary changes
3) scleroderma
a) skin thickening of face & skin distal to elbows & knees
- diffuse disease involves skin proximal to elbows & knees
b) nailfold capillary changes
4) vasculitis
- purpura
- cutaneous nodules
- cutaneous ulcers
5) Behcet syndrome
- oral ulcerations
- genital ulcerations
- erythema nodosum
6) sarcoidosis
- erythema nodosum (including Lofgren's syndrome)
7) psoriatic arthritis
- psoriasis on extensor surfaces, umbilicus, gluteal fold,scalp & behind ears
- pustular psoriasis on palm & soles
- pitting of nails
- onycholysis
8) reactive arthritis including Reiter's syndrome
- psoriaform rash on palms, soles, toes (keratoderma blenorrhagicum)
- psoriaform rash on penis (circinate balanitis)
9) adult-onset Still's disease (juvenile rheumatoid arthritis)
- short-term, pink rash on trunk & proximal extremities
10) rheumatic fever
- erythema marginatum
11) Lyme disease
- erythema chronicum migrans
- acrodermatitis atrophicans (Borrelia afzelii)
Related
rheumatologic disease
skin disease (dermatologic disorder, dermatopathy, dermatosis)
References
- Medical Knowledge Self Assessment Program (MKSAP) 16
American College of Physicians, Philadelphia 2012