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cysteine-rich motor neuron 1 protein (CRIM-1, cysteine-rich repeat-containing protein S52, CRIM1)

Function: 1) role in CNS development by interacting with growth factors implicated in motor neuron differentiation & survival (putative) 2) role in capillary formation & maintenance during angiogenesis (putative) 3) modulates BMP activity by affecting its processing & delivery to the cell surface 4) interacts with BMP4 & BMP7 Structure: - N-glycosylated - contains 4 antistasin-like domains - contains 1 IGFBP domain - contains 6 VWFC domains Compartment: cell membrane, secreted Expression: - expressed in pancreas, kidney, skeletal muscle, lung, placenta, brain, heart, spleen, liver & small intestine - expressed in blood vessels (at protein level)

General

glycoprotein membrane protein

Properties

SIZE: MW = 114 kD entity length = 1036 aa COMPARTMENT: cellular membrane MOTIF: signal sequence {1-34} IGFBP {37-95} MOTIF: N-glycosylation site {N71} N-glycosylation site {N113} Cell attachment site {314-316} N-glycosylation site {N330} VWFC domain {334-391} VWFC domain {401-457} Antistasin-like 1 {469-498} MOTIF: N-glycosylation site {N474} Antistasin-like 2 {505-532} Antistasin-like 3 {539-564} Antistasin-like 4 {567-592} VWFC domain {606-663} VWFC domain {677-735} N-glycosylation site {N746} VWFC domain {751-809} VWFC domain {817-874} transmembrane domain {940-960}

Database Correlations

OMIM 606189 UniProt Q9NZV1 PFAM correlations

References

UniProt :accession Q9NZV1