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complement factor H-related protein 3; FHR-3; DOWN16; H factor-like protein 3 (CFHR3, CFHL3, FHR3)
Function:
- might be involved in complement regulation
Structure: contains 5 Sushi (CCP/SCR) domains
Compartment: secreted
Alternative splicing: named isoforms=2
Expression:
- expressed by the liver & secreted inyo plasma
General
glycoprotein
secreted protein
Properties
SIZE: entity length = 330 aa
MW = 37 kD
COMPARTMENT: extracellular compartment
MOTIF: signal sequence {1-18}
Sushi domain {22-84}
MOTIF: cysteine residue {C23}
MODIFICATION: cysteine residue {C72}
cysteine residue {C55}
MODIFICATION: cysteine residue {C83}
cysteine residue {C72}
MODIFICATION: cysteine residue {C23}
cysteine residue {C83}
MODIFICATION: cysteine residue {C55}
Sushi domain {85-142}
MOTIF: cysteine residue {C87}
MODIFICATION: cysteine residue {C129}
N-glycosylation site {N108}
cysteine residue {C114}
MODIFICATION: cysteine residue {C140}
cysteine residue {C129}
MODIFICATION: cysteine residue {C87}
cysteine residue {C140}
MODIFICATION: cysteine residue {C114}
Sushi domain {144-205}
MOTIF: cysteine residue {C146}
MODIFICATION: cysteine residue {C192}
cysteine residue {C175}
MODIFICATION: cysteine residue {C203}
N-glycosylation site {N185}
cysteine residue {C192}
MODIFICATION: cysteine residue {C146}
cysteine residue {C203}
MODIFICATION: cysteine residue {C175}
N-glycosylation site {N205}
Sushi domain {208-266}
MOTIF: cysteine residue {C210}
MODIFICATION: cysteine residue {C253}
cysteine residue {C239}
MODIFICATION: cysteine residue {C264}
cysteine residue {C253}
MODIFICATION: cysteine residue {C210}
cysteine residue {C264}
MODIFICATION: cysteine residue {C239}
Sushi domain {267-330}
MOTIF: cysteine residue {C268}
MODIFICATION: cysteine residue {C319}
cysteine residue {C302}
MODIFICATION: cysteine residue {C329}
N-glycosylation site {N309}
cysteine residue {C319}
MODIFICATION: cysteine residue {C268}
cysteine residue {C329}
MODIFICATION: cysteine residue {C302}
Database Correlations
OMIM 605336
UniProt Q02985
Pfam PF00084
Entrez Gene 10878
Kegg hsa:10878
References
UniProt :accession Q02985