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chronic pulmonary fibrosis

Etiology: connective tissue disorder Clinical manifestations: 1) indistinquishable from idiopathic pulmonary fibrosis 2) progressive exertional dyspnea presenting months to years after diagnosis of underlying connective tissue disorder Differential diagnosis: 1) esophageal dysfunction with chronic aspiration a) scleroderma b) mixed connective tissue disease 2) respiratory weakness with atelectasis a) systemic lupus erythematosus b) polymyositis c) glucocorticoid-induced myopathy 3) recurrent respiratory tract infection 4) drug-induced interstitial lung disease

General

pulmonary fibrosis chronic lung disease

References

Medical Knowledge Self Assessment Program (MKSAP) 11, American College of Physicians, Philadelphia 1998