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CD4 T lymphocyte deficiency disorder (HIV-negative AIDS)
Etiology: idiopathic
Epidemiology: rare
Pathology:
- immunodeficiency
- susceptibility to opportunistic infections
Laboratory:
- CD4 count is low
Differential diagnosis:
- HIV1 infection
Related
human immunodeficiency virus-1 (HIV-1)
General
lymphocyte disorder
cellular immune dysfunction
References
- Centers for Disease Control and Prevention
Unexplained CD4+ T-Lymphocyte Depletion in Persons Without
Evident HIV Infection -- United States.
MMWR. July 30, 1992 / 41(30);541-545
http://www.cdc.gov/mmwr/preview/mmwrhtml/00017329.htm
- Wikipedia: Idiopathic CD4+ lymphocytopenia
http://en.wikipedia.org/wiki/Idiopathic_CD4%2B_lymphocytopenia
- Luo L, Li T.
Idiopathic CD4 lymphocytopenia and opportunistic infection--
an update.
FEMS Immunol Med Microbiol. 2008 Dec;54(3):283-9.
PMID: 19049641