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A disintegrin & metalloproteinase with thrombospondin type 1 motif 18; ADAMTS-18; ADAM-TS 18; ADAM-TS18 (ADAMTS18, ADAMTS21)

Function: - precursor is cleaved by a furin endopeptidase Cofactor: binds 1 Zn+2 per subunit (putative) Structure: - the conserved Cys present in the cysteine-switch motif binds the catalytic Zn+2, thus inhibiting the enzyme - dissociation of Cys from Zn+2 upon the activation- peptide release activates the enzyme - contains 1 disintegrin domain - contains 1 peptidase M12B domain - contains 1 PLAC domain - contains 5 TSP type-1 domains Compartment: - secreted, extracellular space, extracellular matrix (putative) Alternative splicing: named isoforms=2 Expression: - expressed in fetal lung, liver, & kidney & in adult brain, prostate, submaxillary gland, & endothelium

General

A disintegrin & metalloproteinase with thrombospondin type 1 motif (ADAMTS) glycoprotein

Properties

SIZE: entity length = 1221 aa MW = 135 kD COMPARTMENT: extracellular compartment MOTIF: signal sequence {1-47} N-glycosylation site {N151} N-glycosylation site {N190} Cysteine switch {252-259} MOTIF: Zn+2-binding site SITE: 254-254 Peptidase M12B {293-498} MOTIF: N-glycosylation site {N313} cysteine residue {C414} MODIFICATION: cysteine residue {C493} Zn+2-binding site SITE: 436-436 glutamate residue {E437} Zn+2-binding site SITE: 440-440 Zn+2-binding site SITE: 446-446 cysteine residue {C453} MODIFICATION: cysteine residue {C477} cysteine residue {C477} MODIFICATION: cysteine residue {C453} cysteine residue {C493} MODIFICATION: cysteine residue {C414} disintegrin domain {498-577} TSP1 module {589-644} MOTIF: cysteine residue {C601} MODIFICATION: cysteine residue {C638} cysteine residue {C605} MODIFICATION: cysteine residue {C643} cysteine residue {C616} MODIFICATION: cysteine residue {C628} cysteine residue {C628} MODIFICATION: cysteine residue {C616} cysteine residue {C638} MODIFICATION: cysteine residue {C601} cysteine residue {C643} MODIFICATION: cysteine residue {C605} cysteine-rich region {644-749} MOTIF: N-glycosylation site {N745} Spacer {750-876} MOTIF: N-glycosylation site {N838} N-glycosylation site {N909} TSP1 module {931-990} TSP1 module {991-1049} TSP1 module {1052-1116} TSP1 module {1123-1178} PLAC {1184-1221}

Database Correlations

OMIM 607512 UniProt Q8TE60 PFAM correlations Entrez Gene 170692 Kegg hsa:170692

References

UniProt :accession Q8TE60