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apolipoprotein B mRNA editing enzyme complex

Function: - postranscriptional editing of a CAA codon for Gln to a UAA codon for stop in APOB mRNA - apolipoprotein B mRNA editing results in formation of apo B48, rather than apo B100 - catalytic subunit, APOBEC1, binds to the mRNA & deaminate its target cytosine to uracil - protects the edited APOB mRNA from nonsense-mediated decay Structure: - subunits include: APOBEC1, ACF Expression: mRNA editing of apoB occurs in small intestine

Related

apolipoprotein B mRNA editing enzyme complex (GO:0030895)

General

molecular complex

Properties

SUBUNITS: apo B mRNA-editing protein COMPARTMENT: cytoplasm CELL: epithelial cell WITHIN: small intestine MOTIF: Zn+2-binding site SITE: 61-61 glutamate residue {E63} Zn+2-binding site SITE: 93-93 Zn+2-binding site SITE: 96-96 APOBEC1 complementation factor COMPARTMENT: cytoplasm cell nucleus endoplasmic reticulum MOTIF: RNP motif NAME: RNP motif SITE: 56-134 FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif NAME: ribonucleoprotein-1 motif FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif ribonucleoprotein-2 motif ribonucleoprotein-2 motif FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif ribonucleoprotein-2 motif RNP motif NAME: RNP motif SITE: 136-218 FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif NAME: ribonucleoprotein-1 motif FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif ribonucleoprotein-2 motif ribonucleoprotein-2 motif FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif ribonucleoprotein-2 motif RNP motif NAME: RNP motif SITE: 231-303 FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif NAME: ribonucleoprotein-1 motif FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif ribonucleoprotein-2 motif ribonucleoprotein-2 motif FOR-BINDING-OF: ribonucleic acid MOTIF: ribonucleoprotein-1 motif ribonucleoprotein-2 motif nuclear localization {360-409}

References

  1. UniProt :accession Q9NZI8
  2. Scott et al Current Opinion In Lipidology 5:87 1994

Components

apo B mRNA-editing protein (HEPR, APOBEC1) APOBEC1 complementation factor; APOBEC1-stimulating protein; apo B mRNA-targeting protein (ACF, ASP, A1CF)