aortic subvalvular stenosis

Classification: - two major types: 1) discrete or membranous 2) fibromuscular (fixed or dynamic) (hypertrophic cardiomyopathy) Etiology: congenital malformation Pathology: 1) commonly associated with aortic regurgitation 2) high pressure gradient from left ventricle to aorta Clinical manifestations: 1) prominent left ventricle 2) reduced pulse pressure 3) no ejection click 4) arterial thrill when stenosis is severe 5) hypertrophic obstructive cardiomyopathy a) ejection murmur at left sternal border b) prominent pulses with a bifid quality Radiology: 1) 2-D & doppler echocardiography 2) left heart cardiac catheterization

Related

aortic valvular stenosis (AS) hypertrophic cardiomyopathy (HCM), including idiopathic hypertrophic subaortic stenosis (IHSS)

References

Mayo Internal Medicine Board Review, 1998-99, Prakash UBS (ed) Lippincott-Raven, Philadelphia, 1998, pg 39-40