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aldehyde dehydrogenase 1 family, member A1 (ALDH1A1, aldehyde dehydrogenase 1, aldehyde dehydrogenase cytosolic, RalDH1, ALDH-E1, LDC, ALDH1, PUMB1)
Function:
- binds free retinaldehyde & retinaldehyde bound to cellular retinol-binding protein
- can convert/oxidize retinaldehyde to retinoic acid
- retinoic acid biosynthesis
retinaldehyde + NAD+ + H2O retinoate + NADH
Structure:
- homotetramer
- belongs to the aldehyde dehydrogenase family
Compartment: cytoplasm
Related
aldehyde dehydrogenase-1 gene
General
aldehyde dehydrogenase
oligomerizing protein
Properties
SIZE: entity length = 501 aa
MW = 55 kD
COMPARTMENT: cytoplasm
MOTIF: Transition state stabilizer {170-170}
glutamate residue {E269}
cysteine residue {C303}
cofactor-binding site [456-456]
COFACTOR-BOUND: NAD
Database Correlations
OMIM 100640
UniProt P00352
Pfam PF00171
Entrez Gene 216
Kegg hsa:216
ENZYME 1.2.1.36
References
- OMIM :accession 100640
- UniProt :accession P00352