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visceral heterotaxy X-linked type 1
Genetics:
- associated with defects in ZIC3
Clinical manifestations:
- dextrocardia
- corrected transposition of great arteries
- ventricular septal defect
- patent ductus arteriosus
- pulmonic stenosis
- situs inversus viscerum
- asplenia &/or polysplenia
General
visceral heterotaxy
Database Correlations
OMIM 306955
References
OMIM :accession 306955