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T-cell lymphoid neoplasm (T-cell leukemia, T-cell lymphoma)

Genetics: - overexpression of MTCP1 in T-cell leukemia bearing a t(X;14) translocation - chromosomal aberrations involving T-cell receptor alpha/delta loci activating TCL1A are found in chronic T-cell leukemias - translocation t(14;14)(q11;q32) - translocation t(7;14)(q35;q32) - inversion inv(14)(q11;q32) - TCL6 activated in T-cell leukemias with rearrangements at chromosome 14q32.1 - TNG2 activated in T-cell leukemias with rearrangements at chromosome 14q32.1 - translocations associated with TCTA - chromosomal translocation t(X;14)(q28;q11) involving BRCC3 with TCRA - overexpression of BCL11B, RBM5 - other implicated genes PCM1, TREML2 Laboratory: - see ARUP consult [1]

Interactions

disease interactions

Specific

hepatosplenic T-cell lymphoma (HSTCL) peripheral T-cell lymphoid neoplasm precursor T-cell lymphoid neoplasm

General

non-Hodgkin's lymphoma

References

  1. ARUP Consult: T-Cell/NK-Cell Lymphomas The Physician's Guide to Laboratory Test Selection & Interpretation https://www.arupconsult.com/content/lymphomas-t-cellnk-cell
  2. Horwitz, SM, Ansell SM, Ai WZ, et al. NCCN Guidelines Insights: T-Cell Lymphomas, Version 2.2018. J Natl Compr Canc Netw. 2018 Feb;16(2):123-135. PMID: 29439173 http://www.jnccn.org/content/16/2/123.long