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syndromic microphthalmia 3

Genetics: - associated with defects in SOX2 Clinical manifestations: - association of microphthalmia or clinical anophthalmia with anomalies such as microcephaly, short stature, hypogonadotropic hypogonadism, esophageal atresia & neurologic manifestations

General

microphthalmia (nanophthalmos)

Database Correlations

OMIM 206900

References

UniProt :accession P48431