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SLIT & NTRK-like protein 1 (leucine-rich repeat-containing protein 12, SLITRK1, KIAA1910, LRRC12, UNQ233/PRO266)

Function: - enhances neuronal dendrite outgrowth Structure: - belongs to the SLITRK family - contains 13 LRR repeats (leucine-rich repeats) Compartment: membrane Expression: - expressed predominantly in cerebral cortex, frontal lobe - at 20 weeks of gestation, expressed in multiple brain regions, including developing neo-cortical plate, subplate zone, striatum, globus pallidus, thalamus & subthalamus Pathology: - expressed in some astrocytic brain tumors, astrocytomas, oligodendrogliomas, glioblastomas, gangliogliomas, primitive neuroectodermal tumors - defects in SLITRK1 may be a cause of Gilles de la Tourette syndrome

General

membrane protein SLIT & NTRK-like protein (SLITRK)

Properties

SIZE: MW = 78 kD entity length = 696 aa COMPARTMENT: cellular membrane MOTIF: signal sequence {1-17} leucine-rich repeat SITE: 57-80 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 81-104 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 105-128 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 130-152 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 153-176 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 178-200 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 214-237 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 374-397 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 399-421 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 423-445 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 446-469 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 470-493 MOTIF: leucine residue (SEVERAL) leucine-rich repeat SITE: 495-517 MOTIF: leucine residue (SEVERAL) transmembrane domain {623-643}

Database Correlations

OMIM 137580 UniProt Q96PX8 Pfam PF00560

References

UniProt :accession Q96PX8