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rhizomelic chondrodysplasia punctata, type 3

Pathology: - rhizomelic shortening of femur & humerus - vertebral disorders - cataracts - cutaneous lesions - severe mental retardation Genetics: - mutation in gene for alkyldihydroxyacetonephosphate synthase (AGPS)

General

rhizomelic chondrodysplasia punctata

Database Correlations

OMIM 600121

References

OMIM :accession 600121