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Poland syndrome
Etiology:
- idiopathic
Epidemiology:
- rare
Clinical manifestations:
- unilateral absence or underdevelopment of chest-wall muscles & limb abnormalities, including syndactyly or brachydactyly
- case of absent right pectoralis major & brachydactyly of the right hand (case with report with images) [1]
- muscle strenth intact
* images [1]
Management:
- plastic surgery be of benefit
- physical therapy may improve functionality
General
syndrome
References
- Kennedy KR, Wang AL.
Poland Syndrome
N Engl J Med 2018; 378:72. January 4, 2018
PMID: 29298145
http://www.nejm.org/doi/full/10.1056/NEJMicm1709713?query=TOC