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platyspondylic lethal skeletal dysplasia (PLSD-SD)

Genetics: - associated with defects in FGFR3 Clinical manifestations: - postnatal growth deficiency - mild developmental delay - short trunk - craniofacial abnormalities - platyspondyly - delayed ossification - generalized osteoporosis - thin ribs

General

platyspondylic lethal skeletal dysplasia (PLSD)

References

UniProt :accession P22607