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obliterative portal venopathy

Pathology: - lesions of the intrahepaticbranches of the portal vein - occlusion or obliteration ofsmall branches of the portal vein - may be responsible for many cases of portal hypertension in the absence of cirrhosis or obstruction of large portal veins or hepatic veins Genetics: - associated with defects in C4orf54 (FOPV) - autosomal dominant with incomplete penetrance & variable expressivity

General

venous disease; venopathy

Database Correlations

OMIM 617881

References

  1. UniProt :accession D6RIA3
  2. OMIM :accession 617881