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neuroinflammatory disease
Etiology:
- demyelinating disease
- multiple sclerosis,
- acute disseminated encephalomyelitis
- neuromyelitis optica spectrum disorder
- myelin oligodendrocyte glycoprotein disease
- glial fibrillary acidic protein astrocytopathy
- CNS vasculitis
- multisystem disorders
- neuro-sarcoidosis
- Behcet disease
Laboratory:
- CSF analysis
Radiology:
- neuroimaging: magnetic resonance imaging with gadolinium contrast
Differential diagnosis:
- genetic disorders
- leukodystrophies
- hemophagocytic lymphohistiocytosis
- genetic vasculopathies
Interactions
disease interactions
Specific
demyelinating disease
glial fibrillary acidic protein astrocytopathy
isolated (primary) central nervous system vasculitis (angiitis) (PACNS)
myelin oligodendrocyte glycoprotein antibody-associated disease (MOGAD)
General
inflammation
neurologic disease
References
- Ayrignac X, Carra-Dalliere C, Marelli C et al
Adult-Onset Genetic Central Nervous System Disorders Masquerading
as Acquired Neuroinflammatory Disorders. A Review.
JAMA Neurol. 2022;79(10):1069-1078
PMID: 35969413
https://jamanetwork.com/journals/jamaneurology/fullarticle/2795401