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myxopapillary ependymoma
Epidemiology:
- tend to be located in conus/cauda equina/filum terminale region
- most common intramedullary neoplasm in this region
- can occur in cervical-thoracic cord, lateral ventricle, brain parenchyma
- age range 6 to 82 years
Microscopic Pathology:
- cuboidal to elongated uniform cells
- radial arrangement in papillary manner around vascularized stromal cores
- mucoid matrix
- microcysts
- mitoses low to absenthistopathology
Electron microscopy:
- complex interdigitations
- abundant basement membrane structures
- few cilia
- aggregation of microtubules within rough ER complexes
Immunohistochemistry: GFAP + S 100 + vimentin + cytokeratin -
Clinical manifestations:
- back pain, often long duration
Radiology:
- MRI: circumscribed enhancing lesion
Differential diagnosis:
- chordoma
- myxoid chondrosarcoma
- paraganglioglioma
- mesothelioma
- papillary adenocarcinoma
- pilocytic/pilomyxoid astrocytoma
- chordoid glioma
General
ependymal neoplasm
References
- WHO Classification Tumours of the Nervous System.
Kleihues & Cavenee eds. IARC Press 2000
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