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multicentric reticulohistiocytosis; lipoid dermatoarthritis
Etiology: may be associated with underlying malignancy
Clinical manifestations:
1) most patients have skin lesions & arthritis
2) skin
a) red-brown papules & nodules
b) most commonly on dorsal aspect of hands & on face
3) mucosa
a) 50% of patients
b) lips, buccal mucosa, tongue, gingiva, or nasal mucosa
4) joints - arthritis:
a) severely destructive & mutilating
b) interphalangeal joints of hand
1] 'opera glass hand'
2] 'telecsope fingers
c) knees
d) wrists
e) hips
f) ankles
g) feet
h) elbows
i) spine
5) bones
6) viscera
General
histiocytosis
References
- Mayo Internal Medicine Board Review, 1998-99, Prakash UBS (ed)
Lippincott-Raven, Philadelphia, 1998, pg 176
- KP-CMT, Snomed