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long QT syndrome type 2
Genetics:
- associated with defects in KCNH2
Clinical manifestations:
- syncope & sudden death in response to exercise or emotional stress
- deafness is often associated
Special laboratory:
- electrocardiogram
a) prolonged QT interval
b) polymorphic ventricular arrhythmias
Interactions
disease interactions
General
long QT syndrome
Database Correlations
OMIM 152427
MORBIDMAP 152427
References
OMIM :accession 152427