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long QT syndrome type 11 (LQT11)
Genetics:
- associated with defects in AKAP9
Clinical manifestations:
- syncope & sudden death in response to excercise or emotional stress
- may present as sudden cardiac death in infancy
Special laboratory:
- electrocardiogram:
a) prolonged QT interval
b) polymorphic ventricular arrhythmias
Interactions
disease interactions
General
long QT syndrome
Database Correlations
OMIM 611820
References
OMIM :accession 611820