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long QT syndrome type 10
Genetics:
- associated with defects in SCN4B
Clinical manifestations:
- syncope & sudden death in response to excercise or emotional stress
- may present as sudden cardiac death in infancy
Special laboratory:
- electrocardiogram:
a) prolonged QT interval
b) polymorphic ventricular arrhythmias
Interactions
disease interactions
General
long QT syndrome
Database Correlations
OMIM 611819
References
OMIM :accession 611819