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Figure: urea cycle
- urea cycle 1
- enzyme: carbamoyl phosphate synthase NH3
- substrate: CO2 + NH3 + 2 ATP
- product: carbamoyl phosphate + 2 ADP + H2PO4-
- urea cycle 2
- enzyme: ornithine carbamoyltransferase
- substrate: ornithine + carbamoyl_phosphate
- product: citrulline + H2PO4-
- urea cycle 3
- enzyme: argininosuccinate synthetase
- substrate: citrulline + aspartate + ATP
- product: argininosuccinate + AMP + H2P2O7-2
- urea cycle 4
- enzyme: argininosuccinate lyase
- substrate: argininosuccinate
- product arginine + fumarate
- urea cycle 5
- enzyme: arginase-1
- substrate: arginine + H2O
- product: ornithine + urea
References
- http://www.genome.ad.jp/kegg/pathway/map/map00220.html
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