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familial intrahepatic cholestasis 2

Pathology: - intrahepatic cholestasis Genetics: - associated with defects in ABCB11 Clinical manifestations: - inherited liver disease of childhood Laboratory: - normal serum gamma-glutamyltransferase activity

General

familial intrahepatic cholestasis

Database Correlations

OMIM 601847

References

OMIM :accession 601847