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complement-3 (C3)

Held in a strained configuration by thioester Cys-338 - Glu-341 in alpha chain; alpha & beta chains linked by disulfide bridge. Defects in complement C3: 1) etiology a) congenital liver disease b) systemic lupus erythematosus 2) pathogens a) Staphylococcus aureus b) Streptococcus pneumonia c) Pseudomonas species d) Proteus species

Interactions

molecular events

Related

complement C3 in serum complement cascade

Specific

complement C3a complement C3b complement C3c complement C3d complement C3dg complement C3f complement C3g complement C3[H2O] (iC3)

General

acute phase protein beta 2 globulin complement glycoprotein multisubunit protein

Properties

SIZE: MW = 195 kD COMPARTMENT: plasma MOTIF: glycosylation site SUBUNITS: complement C3-alpha chain :STATE Inactive complement C3-beta chain MISC-INFO: CONCENTRATION 60-140 MG/DL

Database Correlations

OMIM 120700 MORBIDMAP 120700 UniProt P01024

References

  1. Tietz Fundametals of Clinical Chemistry 3rd ed, WB Saunders, 1987 pg 327
  2. Clinical Diagnosis and Management by Laboratory Methods, 18th ed, J.B. Henry (ed), W.B. Saunders, Philadelphia, PA, 1991 pg 832
  3. Harrison's Principles of Internal Medicine, 13th ed. Isselbacher et al (eds), McGraw-Hill Inc. NY, 1994, pg 497

Components

complement C3-alpha chain complement C3-beta chain