Contents

Search


combined oxidative phosphorylation deficiency type 4 (COXPD4)

Pathology: - neonatal lactic acidosis - rapidly progressive encephalopathy - severely decreased mitochondrial protein synthesis - combined deficiency of mtDNA-related mitochondrial respiratory chain complexes Genetics: - associated with defects in TUFM

General

combined oxidative phosphorylation deficiency (COXPD)

Database Correlations

OMIM 610678

References

UniProt :accession P49411