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bronchopulmonary sequestration
Pathology:
- a segment of non-functional lung tissue not connected to the bronchial tree
- does not receive itw blood supply from the pulmonary circulation
- can manifest as a large, vascular lower-lobe consolidation
- generally no communication with upper airway
- bacteria may gain access to sequestration through lower pulmonary connections
Clinical manifestations:
- recurrent pneumonia
Radiology:
- chest CT:
- an anomalous systemic artery is visible in 2/3 of patients
- origin most frequently thoracic aorta
- origin less frequently abdominal aorta or coronay artery
- MRI of thorax may be necessary for diagnosis
General
congenital lung disease; congenital lung malformation
References
- Shanmugam G
Adult congenital lung disease
Eur J Cardiothorac Surg. 2005 Sep;28(3):483-9.
PMID: 15975811
- Garcia-Pena P, Coma A, Enriquez G
Congenital lung malformations: radiological findings and clues for differential
diagnosis.
Acta Radiol. 2013 Nov;54(9):1086-95
PMID: 23436824 Review.