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blue rubber bleb nevus

Painful/tender, compressible blue swelling in variant of capillary venous lymphatic malformation (cavernous hemangioma). Clinical manifestations: 1) Tender, compressible blue swelling 2) size: a few mm to several cm 3) may exhibit localized hyperhidrosis 4) often occurs multiply on trunk & upper arms 5) similar lesions may occur in the GI tract * images [2] Complications: - hemorrhage from GI lesions

Related

Maffucci's syndrome

General

cavernous hemangioma (cavernoma, capillary venous lymphatic malformation, CVL, nevus cavernosus, vascular erectile tumor)

Database Correlations

OMIM 112200

References

  1. Color Atlas & Synopsis of Clinical Dermatology, Common & Serious Diseases, 3rd ed, Fitzpatrick et al, McGraw Hill, NY, 1997, pg 154-55
  2. DermNet NZ. Venous malformation (images) http://www.dermnetnz.org/vascular/venous-malformation.html