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autoimmune encephalomyelitis
Etiology:
- NMDA receptor autoantibody
Laboratory:
- NMDA receptor IgG in CSF
- see ARUP consult [1]
Differential diagnosis:
- insidious onset, positive nonspecific serum antibodies suggest other diagnosis [2]
Specific
experimental autoimmune encephalomyelitis
paraneoplastic encephalomyelitis sensory neuropathy
General
encephalomyelitis
References
- ARUP Consult: N-methyl-D-Aspartate (NMDA) type
Glutamate Receptor Autoantibody Disorders
Anti-NMDA-Receptor Encephalitis
The Physician's Guide to Laboratory Test Selection & Interpretation
https://www.arupconsult.com/content/n-methyl-d-aspartate-nmda-type-glutamate-receptor-autoantibody-disorders
- Anti-NMDA Receptor (NR1) IgG Antibodies
https://arupconsult.com/ati/anti-nmda-receptor-nr1-igg-antibodies
- Flanagan EP et al.
Autoimmune encephalitis misdiagnosis in adults.
JAMA Neurol 2022 Nov 28; [e-pub].
PMID: 36441519 PMCID: PMC9706400 Free PMC article
https://jamanetwork.com/journals/jamaneurology/fullarticle/2799083