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acylcarnitine in serum/plasma

Indications: - suspected - fatty acid oxidation disorders - carnitine deficiency - disorders of carnitine metabolism - organic acidemias Specimen: - whole blood: 1 mL Green Top (Heparin), Red top or Gold Top - spin & freeze at least 200 uL of heparinized plasma or serum - ship frozen on dry ice

Related

acylcarnitine carnitine in serum/plasma

Specific

3-hydroxydodecanoylcarnitine in serum/plasma 3-hydroxyisovalerylcarnitine in serum/plasma 3-hydroxylinoleoylcarnitine in serum/plasma 3-hydroxyoleoylcarnitine in serum/plasma 3-hydroxypalmitoleylcarnitine in serum/plasma 3-hydroxypalmitoylcarnitine in serum/plasma 3-hydroxystearoylcarnitine in serum/plasma 3-hydroxytetradecanoylcarnitine in serum/plasma 3-hydroxytetradecenoylcarnitine in serum/plasma acetylcarnitine in serum/plasma benzoylcarnitine in serum/plasma butyrylcarnitine in serum/plasma crotonylcarnitine in serum/plasma decanoylcarnitine in serum/plasma decenoylcarnitine in serum/plasma dicarboxyoleylcarnitine in serum/plasma dodecanoylcarnitine in serum/plasma dodecenoylcarnitine in serum/plasma glutarylcarnitine in serum/plasma hexanoylcarnitine in serum/plasma isovalerylcarnitine + methylbutyrylcarnitine in serum/plasma isovalerylcarnitine in serum/plasma linoleoylcarnitine in serum/plasma methylmalonylcarnitine in serum/plasma octanoylcarnitine in serum/plasma octenoylcarnitine in serum/plasma oleoylcarnitine in serum/plasma palmitoleylcarnitine in serum/plasma palmitoylcarnitine in serum/plasma propionylcarnitine in serum/plasma stearoylcarnitine in serum/plasma suberylcarnitine in serum/plasma tetradecadienoylcarnitine in serum/plasma tetradecanoylcarnitine in serum/plasma tetradecenoylcarnitine in serum/plasma

General

special chemistry test

References

  1. Seattle Children's Hospital Diagnostic Services, Genetics Lab http://www.seattlechildrens.org/healthcare-professionals/access/diagnostic-services/genetics-lab/TestDetails.aspx?TestId=175
  2. Panel of 4 tests Laboratory Test Directory ARUP: 80068
  3. Panel of 34 tests Laboratory Test Directory ARUP: 81110

Component-of

acylcarnitines/carnitine free in serum/plasma carnitine/acylcarnitine in serum/plasma