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acylcarnitine in serum/plasma
Indications:
- suspected
- fatty acid oxidation disorders
- carnitine deficiency
- disorders of carnitine metabolism
- organic acidemias
Specimen:
- whole blood: 1 mL Green Top (Heparin), Red top or Gold Top
- spin & freeze at least 200 uL of heparinized plasma or serum
- ship frozen on dry ice
Related
acylcarnitine
carnitine in serum/plasma
Specific
3-hydroxydodecanoylcarnitine in serum/plasma
3-hydroxyisovalerylcarnitine in serum/plasma
3-hydroxylinoleoylcarnitine in serum/plasma
3-hydroxyoleoylcarnitine in serum/plasma
3-hydroxypalmitoleylcarnitine in serum/plasma
3-hydroxypalmitoylcarnitine in serum/plasma
3-hydroxystearoylcarnitine in serum/plasma
3-hydroxytetradecanoylcarnitine in serum/plasma
3-hydroxytetradecenoylcarnitine in serum/plasma
acetylcarnitine in serum/plasma
benzoylcarnitine in serum/plasma
butyrylcarnitine in serum/plasma
crotonylcarnitine in serum/plasma
decanoylcarnitine in serum/plasma
decenoylcarnitine in serum/plasma
dicarboxyoleylcarnitine in serum/plasma
dodecanoylcarnitine in serum/plasma
dodecenoylcarnitine in serum/plasma
glutarylcarnitine in serum/plasma
hexanoylcarnitine in serum/plasma
isovalerylcarnitine + methylbutyrylcarnitine in serum/plasma
isovalerylcarnitine in serum/plasma
linoleoylcarnitine in serum/plasma
methylmalonylcarnitine in serum/plasma
octanoylcarnitine in serum/plasma
octenoylcarnitine in serum/plasma
oleoylcarnitine in serum/plasma
palmitoleylcarnitine in serum/plasma
palmitoylcarnitine in serum/plasma
propionylcarnitine in serum/plasma
stearoylcarnitine in serum/plasma
suberylcarnitine in serum/plasma
tetradecadienoylcarnitine in serum/plasma
tetradecanoylcarnitine in serum/plasma
tetradecenoylcarnitine in serum/plasma
General
special chemistry test
References
- Seattle Children's Hospital
Diagnostic Services, Genetics Lab
http://www.seattlechildrens.org/healthcare-professionals/access/diagnostic-services/genetics-lab/TestDetails.aspx?TestId=175
- Panel of 4 tests
Laboratory Test Directory ARUP: 80068
- Panel of 34 tests
Laboratory Test Directory ARUP: 81110
Component-of
acylcarnitines/carnitine free in serum/plasma
carnitine/acylcarnitine in serum/plasma